Diabetes insipidus, následovaný po 4 letech dysartrií a lehkou pravostrannou hemiparézou - první klinické příznaky Erdheimovy-Chesterovy nemoci. Popis a zobrazení případu s přehledem informací o této nemoci

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Title in English Diabetes insipidus followed after 4 years dysarthria and light dextral hemiparesis - 1st symptom of Erdheim-Chester's disease. A casuistry.
Authors

ADAM Zdeněk BALŠÍKOVÁ Karola POUR Luděk KREJČÍ Marta SVAČINA P. DUFEK Michal KŘEN Leoš HERMANOVÁ Markéta MOULIS Mojmír VANÍČEK Jiří NEUBAUER Jiří MECHL Marek PRÁŠEK Jiří STANÍČEK J. KOUKALOVÁ R. HÁJEK Roman MAYER Jiří

Year of publication 2009
Type Article in Periodical
Magazine / Source Vnitřní lékařství
MU Faculty or unit

Faculty of Medicine

Citation
Field Oncology and hematology
Keywords Diabetes insipidus;Erdheim-Chester's disease; multiple myeloma
Description This casuistry is focused on one pacitent with Erdheim-Chester's disease and with clinical symptom of diabetes insipidus.In 2004, diabetes insipidus was the first clinical sign of Erdheim-Chester disease in our patient. Following introduction of substitution therapy with adiuretin, the patient had no further health complaints for four years until 2008 when he gradually developed dysarthria and, consequently, movement disorder in the form of mild right hemiparesis. The first CNS CT scan (2004) did not reveal any pathology. The first pathological MRI of the brain in 2006 - thickening of pituitary stalk by pathological infiltration to 4-5 mm. During the following year, further infiltrates were detected in the CNS. The number and size of CNS infiltrates increased gradually on MRIs performed repeatedly up to 2008. Erdheim-Chester disease has become suspected based on PET-CT examination at the end of 2008.
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